Noncompaction Cardiomyopathy by Kadir Caliskan & Osama I. Soliman & Folkert J. ten Cate

Author:Kadir Caliskan & Osama I. Soliman & Folkert J. ten Cate
Language: eng
Format: epub
ISBN: 9783030177201
Publisher: Springer International Publishing

Fig. 6.2 Colour Doppler echocardiographic images demonstrating intertrabecular recesses (see white arrows)

Fig. 6.3Routine electrocardiography demonstrating normofrequent sinus rhythm without significant arrhythmia or conductance disorder

Prevalence of Noncompaction Cardiomyopathy

The true prevalence of NCCM in the general population would be determined based on population-based echocardiographic screening. However, there are no population-based studies to determine the real prevalence of NCCM [1]. The first prospective and large echocardiography-based study to determine the real prevalence of NCCM has just been published [1]. This prospective case-control study included all subjects who underwent a transthoracic echocardiogram in an academic center within one-year [1]. From 10,857 echocardiograms performed, 26 cases of NCCM were detected giving an estimated prevalence of 0.24% for this cohort [1]. Most patients (77%) had ≤50% LV ejection fraction in higher ages. When cases with dilated cardiomyopathies of different aetiologies were analysed, 6.8% of the cases showed NCCM with EF <50%. When only those patients with idiopathic dilated cardiomyopathy were included, the estimated prevalence of NCCM was 24%. When LV noncompaction was detected only incidentally in an otherwise healthy and asymptomatic population with normal ejection fraction, the prevalence was 0.05% [1]. In a recent study by Ivanov et al., a cohort of 700 patients referred for cMRI underwent diagnostic assessment for NCCM by four separate imaging criteria referenced by their authors as Petersen, Stacey, Jacquier, and Captur, with a NCCM prevalence of 39%, 23%, 25% and 3%, respectively [9]. In the childhood, large paediatric studies have found NCCM to be the most common form of unclassified cardiomyopathies [10, 11].

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